ROSAI-DORFMAN DISEASE: A CASE STUDY AND LITERATURE REVIEW

Abstract

Rosai-Dorfman Disease (RDD) is a disorder that does not occur commonly; involving the macrophages of the body, characterized by histiocytosis and general lymphadenopathy (especially involving the cervical lymph nodes). Its involvement is divided broadly into two categories: nodal and extra-nodal. A case of this rare disease presented in the surgical department of the Pakistan Institute of Medical Sciences (PIMS). She was a 13- year-old female who had been experiencing respiratory signs and symptoms for the last 2-3 years, had multiple visits to various hospitals, and even had multiple pleural taps to relieve her pulmonary symptoms. She came to the general surgery department when her symptoms were aggravating and there was no drainage via a chest tube already in place. She received apt treatment for her disease including Video-Assisted Thoracic Surgery (VATS) and decortication of pleural scar tissue. She was discharged on 12th post-op. day with no post-operative complications and instructions to have follow-ups with her physicians.